Št. zadetkov: 19
Diplomsko delo
Oznake:
gozdovi;drevesa;sečnja;nezakonita sečnja;ekološka kriminaliteta;trgovina z lesom;diplomske naloge;
Nelegalno izsekavanje gozdov in trgovina z lesom je ena izmed vrst organizirane ekološke kriminalitete in je razširjena po celem svetu. Ta vrsta kriminalitete postaja vse večji problem, saj je v porastu glede na analizo primerov, ki sem jih pridobil od »Illegal-logging.info«. Negativen vpliv se kaže ...
Leto:
2012
Vir:
Fakulteta za varnostne vede (UM FVV)
Magistrsko delo
Oznake:
droge;prepovedane droge;preprečevanje;magistrska dela;
Trgovina z drogo je kot ena izmed temeljnih dejavnosti organiziranega kriminala razširjena po celem svetu. Trg drog oziroma tihotapljenje in preprodaja prepovedanih drog postajata vse večji problem, saj sta v porastu. Poleg tega se na trgu drog vsako leto pojavijo nove psihoaktivne snovi. Še vedno s ...
Leto:
2015
Vir:
Fakulteta za varnostne vede (UM FVV)
Izvirni znanstveni članek
Oznake:
ANA;biologic therapy;HLA B27;juvenile idiopathic arthitis;long-term follow-up;methotrexate;oligoarthritis;outcome;pediatric arthritis;
Background: To evaluate long-term outcomes and prognostic factors in patients with juvenile idiopathic arthritis (JIA), presenting as oligoarthritis, who received IAC as the first treatment for their disease. Methods: We conducted retrospective study at the University Children's Hospital Ljubljana, ...
Leto:
2024
Vir:
Digitalni repozitorij raziskovalnih organizacij Slovenije
Izvirni znanstveni članek
Oznake:
adalimumab;cytokines;etanercept;juvenile idiopathic arthritis;tumour necrosis factor-alpha;
Objective: To determine the dynamics of serum levels of TNF-α in patients with juvenile idiopathic arthritis (JIA) treated with anti-TNF-α biological drugs and investigate their association with the disease activity. Methods: We conducted a single-centre, observational cohort study in 98 patients wi ...
Leto:
2024
Vir:
Digitalni repozitorij raziskovalnih organizacij Slovenije
Izvirni znanstveni članek
Oznake:
food allergy;children;adequate nutrition;nitric oxide;physical activity;beetroot;football;
Leto:
2024
Vir:
Digitalni repozitorij raziskovalnih organizacij Slovenije
Štefan Blazina,
Maruša Debeljak,
Mitja Košnik,
Saša Simčič,
Sanja Stopinšek,
Gašper Markelj,
Nataša Toplak,
Peter Kopač,
Breda Zakotnik,
Marko Pokorn,
Tadej Avčin
Izvirni znanstveni članek
Oznake:
complement deficiency;primary immunodeficiency;laboratory analysis;genetic analysis;clinical manifestations;
Background: Prevalence of complement deficiencies (CDs) is markedly higher in Slovenian primary immunodeficiency (PID) registry in comparison to other national and international PID registries.
Objective: The purposes of our study were to confirm CD and define complete and partial CD in registered ...
Leto:
2018
Vir:
Digitalni repozitorij raziskovalnih organizacij Slovenije
Ana Klinc,
Urh Grošelj,
Matej Mlinarič,
Matjaž Homan,
Gašper Markelj,
Ajda Mezek,
Andreja Širca-Čampa,
Jaka Šikonja,
Tadej Battelino,
Mojca Žerjav-Tanšek,
Ana Drole Torkar
Kratki znanstveni prispevek
Oznake:
glycogen storage disease type 1B;GSD-1b;empagliflozin;SGLT2 inhibitor;neutropenia;
Glycogen storage disease type 1b (GSD-1b) is characterized by neutropenia and neutrophil dysfunction generated by the accumulation of 1,5-anhydroglucitol-6-phosphate in neutrophils. Sodium-glucose co-transporter 2 inhibitors, such as empagliflozin, facilitate the removal of this toxic metabolite and ...
Leto:
2024
Vir:
Medicinska fakulteta (UL MF)
Carla Gaggiano,
Mojca Zajc Avramovič,
Antonio Vitale,
Nina Emeršič,
Jurgen Sota,
Nataša Toplak,
Stefano Gentileschi,
Valeria Caggiano,
Maria Tarsia,
Gašper Markelj,
Tina Vesel,
Anja Koren,
Tadej Avčin
Izvirni znanstveni članek
Oznake:
spondyloarthritis;febrile spondyloarthritis;Still’s disease;systemic juvenile idiopathic arthritis;adult-onset Still’s disease;auto-inflammatory diseases;
Objectives. – (1) characterizing a group of spondyloarthritis (SpA) patients with systemic autoinflammatory symptoms (S-SpA); (2) comparing SpA features with and without auto-inflammatory symptoms; (3) comparing the auto-inflammatory features of S-SpA and Still’s disease (SD). Methods. – Retrospecti ...
Leto:
2024
Vir:
Digitalni repozitorij raziskovalnih organizacij Slovenije
Katarina Štajer,
Neja Kovač,
Jaka Šikonja,
Matej Mlinarič,
Sara Bertok,
Jernej Brecelj,
Maruša Debeljak,
Jernej Kovač,
Gašper Markelj,
David Neubauer,
Rina Rus,
Mojca Žerjav-Tanšek,
Ana Drole Torkar,
Aleksandra Zver,
Tadej Battelino,
Rosa Jiménez Torres,
Urh Grošelj
Pregledni znanstveni članek
Oznake:
Phosphoribosylpyrophosphate synthetase 1;PRPS1;PRS-I super-activity;PRS-I deficiency;Arts syndrome;X-linked Charcot-Marie-Tooth neuropathy type 5;
Phosphoribosyl pyrophosphate synthetase 1 (PRS–I) is an enzyme involved in nucleotide metabolism. Pathogenic variants in the PRPS1 are rare and PRS-I deficiency can manifest as three clinical syndromes: X-linked nonsyndromic sensorineural deafness (DFN2), X-linked Charcot-Marie-Tooth neuropathy type ...
Leto:
2023
Vir:
Medicinska fakulteta (UL MF)
Tina Vesel,
Veronika Osterman,
Jerneja Ahčan,
Helena Mole,
Katja Dejak Gornik,
Alenka Biteznik,
Sara Jevnikar,
Larisa Janžič,
Miha Bajc,
Andreja Nataša Kopitar,
Nataša Toplak,
Maša Bizjak,
Maša Bizjak,
Jakob Peterlin,
Tadej Avčin,
Miroslav Petrovec,
Alojz Ihan,
Mojca Zajc Avramovič,
Gašper Markelj
Izvirni znanstveni članek
Oznake:
varicella vaccination;juvenile idiopathic arthritis;biologic therapy;anti-cytokine therapy;
Objective: To evaluate safety, long-term effectiveness and immunogenicity of varicella vaccination in children with JIA, treated with biologic disease-modifying antirheumatic drugs (bDMARDs). Methods: This is a prospective case-control study. VZV-naive patients with JIA on selected bDMARDs (TNFi, IL ...
Leto:
2025
Vir:
Repozitorij Univerze v Ljubljani (RUL)