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Izvirni znanstveni članek
Oznake: autoinfammatory diseases;interleukin-1 mediated diseases;diagnosis;treatment;monitoring;patientreported outcomes;transition;
Background: Global healthcare disparities, stemming from organizational diferences in healthcare systems, lead to variable availability and funding, resulting in a gap between recommended and implemented practices for interleukin (IL)-1-mediated autoinfammatory diseases. We aimed to assess diagnosti ...
Leto: 2025 Vir: Digitalni repozitorij raziskovalnih organizacij Slovenije
Izvirni znanstveni članek
Oznake: macrophage activation syndrome;haemophagocytic syndromes;haemophagocytic lymphohistiocytosis;treatment;
Objective: To assess current treatment in macrophage activation syndrome (MAS) worldwide and to highlight any areas of major heterogeneity of practice. Methods: A systematic literature search was performed in both EMBASE and PubMed databases. Paper screening was done by two independent teams based o ...
Leto: 2025 Vir: Digitalni repozitorij raziskovalnih organizacij Slovenije
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